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The aim of this study is to characterize the role of currently available CT and MRI markers in clinical studies, and to discuss challenges with CF studies.
This study aimed to determine whether breathing 100% oxygen altered tidal breathing parameters in healthy young children and young children with CF.
In this review, we consider recent evidence regarding hypoxia and sterile inflammation in cystic fibrosis airways
Free NE activity is deleterious for epithelial homeostasis and support the hypothesis that proteases in the airway contribute to CF structural lung disease
Lung clearance index may be a useful surveillance tool to monitor structural lung disease in preschool and school-age children with cystic fibrosis
Aspergillus species and P. aeruginosa are commonly present in the lower airways from infancy
The aim of this study is to identify and quantify the preferences of patients with cystic fibrosis regarding treatment outcomes
Acinar ventilation inhomogeneity measured by single-breath washout was not associated with structural lung disease on CT
Structural changes identified on CT scans in primary ciliary dyskinesia are not identical to those previously described in cystic fibrosis patients
Protease elastase exocytosis by airway neutrophils occurs in all cystic fibrosis children, and its cellular measure correlates with early lung damage